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SKU # | PRODUCT # | DESCRIPTION |
NU385789 | 117791 | XLeu Maxamaid; A leucine-free powdered medical food for the dietary management of isovaleric acidemia and other proven disorders of leucine metabolism in children ages 1 to 8 years.Leucine-freeContains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elementsAge-appropriate DRI formulationXLeu Maxamaid provides 25 g of protein equivalent per 100 g of powderAvailable in orange flavorDoes not contain fat thereby allowing greater flexibility in modifying energy intakeIndications:Isovaleric acidemiaOther proven disorders of leucine metabolismIngredients:Sugar, Corn Syrup Solids, L-Proline, Glycine, L-Arginine L-Aspartate, Calcium Phosphate Dibasic, Citric Acid, L-Lysine Acetate, Tripotassium Citrate, Artificial Flavors, L-Glutamine, L-Phenylalanine, L-Tyrosine, L-Alanine, L-Threonine, L-Histidine, L-Serine, Maltodextrin, Disodium Hydrogen Phosphate, L-Valine, L-Cystine, Sodium Chloride, L-Isoleucine, Magnesium Acetate, N-Acetyl L-Methionine, Choline Bitartrate, L-Tryptophan, Magnesium L-Aspartate, Taurine, L-Ascorbic Acid, Tricalcium Phosphate, M-Inositol, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, Calcium D-Pantothenate, Cupric Sulfate, Thiaminee Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Artificial Colors (Beta Carotene, Beet Red), Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin.Precautions:Use only under strict medical supervision. Not for use when planning or during pregnancy.Seek medical advice before using with serotonergic medications.; 454 g; 6 Each / Case | |
NU385786 | 117792 | XPhe Maxamaid - Orange; A phenylalanine-free powdered medical food for the dietary management of phenylketonuria (PKU) in children aged 1 to 8 years.Phenylalanine-freeContains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elementsAge-appropriate DRI formulationXPhe Maxamaid provides 25 g of protein equivalent per 100 g of powder Available in unflavored, orange and strawberry flavorsDoes not contain fat thereby allowing greater flexibility in modifying energy intakeIndications:PhenylketonuriaIngredients:Corn Syrup Solids, L-Arginine L-Aspartate, Calcium Phosphate Dibasic, L-Leucine, L-Tyrosine, Tripotassium Citrate, L-Proline, L-Valine, Glycine, L-Isoleucine, L-Glutamine, L-Threonine, L-Serine, L-Histidine, Maltodextrin, L-Alanine, Disodium Hydrogen Phosphate, Sodium Chloride, Sugar, Magnesium Aceate, L-Cystine, Choline Bitartrate, N-Acetyl LMethionine, L-Tryptohan, Magnesium L-Aspartate, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, Calcium D-Pantothenate, Cupric Sulphate, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin.Unflavored version also contains: 2% or less of Sugar. Orange flavored version also contains: Sugar, Citric Acid, and 2% or less of each of the following: Artificial Flavors, Artificial Colors (Beta Carotene, Beet Red)..Precautions:Use only under strict medical supervision. Not for use when planning or during pregnancy.Seek medical advice before using with serotonergic medications.; 454 g; 6 Each / Case | |
NU385784 | 118303 | XMTVI Analog; A methionine-, threonine-, valine-free and isoleucine-low powdered infant formula for the dietary management of vitamin B12 non-responsive methylmalonic acidemia or propionic acidemia.Methionine-, threonine-, valine-free and isoleucine-lowUnflavored powderContains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium)XMTVI Analog provides 13 g of protein equivalent per 100 g of powderOsmolality (at 15% w/v): 377 mOsm/kgIngredients:Corn Syrup Solids, High Oleic Safflower Oil, Refined Vegetable Oil (Coconut, Soy), L-Lysine L-Glutamate, L-Leucine, Calcium Phosphate Dibasic, L-Alanine, L-Arginine, L-Aspartic Acid, Galactose , L-Histidine, L-Phenylalanine, L-Tyrosine, Tripotassium Citrate, L-Serine, Calcium Phosphate Monobasic, Glycine, L-Proline, Mono and Diglycerides, L-Cystine, L-Tryptophan, Sodium Chloride, Magnesium Acetate, Potassium Chloride, Diacetyl Tartaric Acid Esters of Monoglycerides, Tricalcium Citrate, L-Glutamine, Choline Bitartrate, M-Inositol, L-Ascorbic Acid, L-Glutamic Acid, Soy Lecithin, Calcium Phosphate Tribasic, Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Nicotinamide, DL-Alpha Tocopheryl Acetate, Calcium Pantothenate, Manganese Sulfate, Cupric Sulfate, Vitamin A Acetate, Pyridoxine Hydrochloride, Riboflavin, Thiaminee Chloride Hydrochloride, Chromium Sulfate, Potassium Iodide, Folic Acid, Sodium Molybdate, Phylloquinone, Biotin, Sodium Hydrogen Selenite, Vitamin D3, Cyanocobalamin.Precautions:Use only under strict medical supervision. Not for use when planning or during pregnancy.Seek medical advice before using with serotonergic medications.; 400 g /14 oz; 6 Each / Case | |
NU385782 | 118328 | XLys, XTrp Analog; A lysine- and tryptophan-free powdered infant formula for the dietary management of glutaric acidemia type I. Lysine- and tryptophan-freeUnflavored powderContains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium)XLys, XTrp Analog provides 13 g of protein equivalent per 100 g of powderOsmolality (at 15% w/v) = 377 mOsm/kgIngredients:Corn Syrup Solids, High Oleic Safflower Oil, Refined Vegetable Oil (Coconut, Soy), Calcium Phosphate Dibasic, L-Leucine, L-Glutamic Acid, L-Proline, L-Arginine, L-Valine, Glycine, L-Isoleucine, L-Aspartic Acid, Galactose, L-Threonine, Tripotassium Citrate, L-Phenylalanine, L-Tyrosine, L-Serine, Calcium Phosphate Monobasic, L-Alanine, L-Histidine, Mono and Diglycerides, L-Cystine, Sodium Chloride, L-Methionine, Magnesium Acetate, Potassium Chloride, Diacetyl Tartaric Acid Esters of Monoglycerides, Tricalcium Citrate, L-Glutamine, Choline Bitartrate, M-Inositol, L-Ascorbic Acid, Soy Lecithin, Calcium Phosphate Tribasic, Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Nicotinamide, DL-Alpha Tocopheryl Acetate, Calcium Pantothenate, Manganese Sulfate, Cupric Sulfate, Vitamin A Acetate, Pyridoxine Hydrochloride, Riboflavin, Thiamine Chloride Hydrochloride, Chromium Sulfate, Potassium Iodide, Folic Acid, Sodium Molybdate, Phylloquinone, D-Biotin, Sodium Hydrogen Selenite, Vitamin D3, Cyanocobalamin.Precautions:Use only under strict medical supervision. Not for use when planning or during pregnancy.Seek medical advice before using with serotonergic medications.; 400 g /14 oz; 6 Each / Case | |