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SKU # | PRODUCT # | DESCRIPTION |
NU385784 | 118303 | XMTVI Analog; A methionine-, threonine-, valine-free and isoleucine-low powdered infant formula for the dietary management of vitamin B12 non-responsive methylmalonic acidemia or propionic acidemia.Methionine-, threonine-, valine-free and isoleucine-lowUnflavored powderContains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium)XMTVI Analog provides 13 g of protein equivalent per 100 g of powderOsmolality (at 15% w/v): 377 mOsm/kgIngredients:Corn Syrup Solids, High Oleic Safflower Oil, Refined Vegetable Oil (Coconut, Soy), L-Lysine L-Glutamate, L-Leucine, Calcium Phosphate Dibasic, L-Alanine, L-Arginine, L-Aspartic Acid, Galactose , L-Histidine, L-Phenylalanine, L-Tyrosine, Tripotassium Citrate, L-Serine, Calcium Phosphate Monobasic, Glycine, L-Proline, Mono and Diglycerides, L-Cystine, L-Tryptophan, Sodium Chloride, Magnesium Acetate, Potassium Chloride, Diacetyl Tartaric Acid Esters of Monoglycerides, Tricalcium Citrate, L-Glutamine, Choline Bitartrate, M-Inositol, L-Ascorbic Acid, L-Glutamic Acid, Soy Lecithin, Calcium Phosphate Tribasic, Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Nicotinamide, DL-Alpha Tocopheryl Acetate, Calcium Pantothenate, Manganese Sulfate, Cupric Sulfate, Vitamin A Acetate, Pyridoxine Hydrochloride, Riboflavin, Thiaminee Chloride Hydrochloride, Chromium Sulfate, Potassium Iodide, Folic Acid, Sodium Molybdate, Phylloquinone, Biotin, Sodium Hydrogen Selenite, Vitamin D3, Cyanocobalamin.Precautions:Use only under strict medical supervision. Not for use when planning or during pregnancy.Seek medical advice before using with serotonergic medications.; 400 g /14 oz; 6 Each / Case | |
NU385782 | 118328 | XLys, XTrp Analog; A lysine- and tryptophan-free powdered infant formula for the dietary management of glutaric acidemia type I. Lysine- and tryptophan-freeUnflavored powderContains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium)XLys, XTrp Analog provides 13 g of protein equivalent per 100 g of powderOsmolality (at 15% w/v) = 377 mOsm/kgIngredients:Corn Syrup Solids, High Oleic Safflower Oil, Refined Vegetable Oil (Coconut, Soy), Calcium Phosphate Dibasic, L-Leucine, L-Glutamic Acid, L-Proline, L-Arginine, L-Valine, Glycine, L-Isoleucine, L-Aspartic Acid, Galactose, L-Threonine, Tripotassium Citrate, L-Phenylalanine, L-Tyrosine, L-Serine, Calcium Phosphate Monobasic, L-Alanine, L-Histidine, Mono and Diglycerides, L-Cystine, Sodium Chloride, L-Methionine, Magnesium Acetate, Potassium Chloride, Diacetyl Tartaric Acid Esters of Monoglycerides, Tricalcium Citrate, L-Glutamine, Choline Bitartrate, M-Inositol, L-Ascorbic Acid, Soy Lecithin, Calcium Phosphate Tribasic, Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Nicotinamide, DL-Alpha Tocopheryl Acetate, Calcium Pantothenate, Manganese Sulfate, Cupric Sulfate, Vitamin A Acetate, Pyridoxine Hydrochloride, Riboflavin, Thiamine Chloride Hydrochloride, Chromium Sulfate, Potassium Iodide, Folic Acid, Sodium Molybdate, Phylloquinone, D-Biotin, Sodium Hydrogen Selenite, Vitamin D3, Cyanocobalamin.Precautions:Use only under strict medical supervision. Not for use when planning or during pregnancy.Seek medical advice before using with serotonergic medications.; 400 g /14 oz; 6 Each / Case | |
NU385822 | 90217 | Milupa PKU 2; Milupa PKU 2 Milupa PKU 2 is a powdered medical food containing a mixture of pure L-amino acids free from phenylalanine, and enriched with vitamins, minerals and trace elements. For the dietary management of phenylketonuria (PKU) and hyperphenylalaninemia in children. Milupa PKU 2 - Main Features: Phenylalanine-free Medical Food, based on free amino acids For the dietary management of Phenylketonuria and Hyperphenylalaninemia (PKU/HPA) Enriched with vitamins, minerals, and trace elements Osmolality (mOsm/kg) Dilution 1 to 9 - 790 mOsm/kg Milupa PKU 2 - Indications: Phenylketonuria Hyperphenylalaninemia Milupa PKU 2 - Preparation: The amount of PKU 2 needed to supplement total daily protein requirements (other than phenylalanine) depends on age, body weight, and individual phenylalanine tolerance. The dose of PKU 2 must be determined by a physician or dietitian and adjusted periodically. The daily amount required should be divided into 3 to 5 single portions and can be taken mixed with calculated amounts of other food (e.g. beverages, fruit mousse). For accuracy, PKU 2 should be weighed on a gram scale. Precaution: Must be used under medical supervision. For toddlers, children and adolescents with proven PKU/HPA. Not suitable as a sole source of nutrition. Not for parenteral use. Storage: Store unopened cans at room temperature. Do not store at extreme temperatures. After opening, keep can tightly covered and store in a cool, dry place (not in the refrigerator) and use within four weeks. Ingredients:L-Amino Acids (L-Lysine-L-Glutamate, L-Glutamic Acid, L-Leucine, L-Proline, L-Aspartic Acid, L-Valine, L-Isoleucine, L-Tyrosine, L-Serine, L-Threonine, L-Alanine, L-Arginine, Magnesium-L-Aspartate, L-Histidine, L-Methionine, L-Cystine, Glycine, L-Tryptophan), Sugar, Potassium Phosphate, Calcium Phosphate, Calcium Carbonate, Salt, Choline Bitartrate, Myo-Inositol, Ascorbic Acid, Ferrous Sulphate, Vanillin, Niacinamide, Vitamin EPrecautions:Use only under strict medical supervision. Not for use when planning or during pregnancy.Seek medical advice before using with serotonergic medications.; 500 g / 17.6 oz; 6 Each / Case | |
NU385827 | 659361 | Milupa UCD 2; A powdered medical food for the dietary management of Urea Cycle Disorders in individuals over 1 year of age.Essential amino acidsConcentrated, unflavored powderEnriched with vitamins, minerals and trace elementsOsmolality (at a 1 to 9 dilution): 810 mOsm/kgIndications:Carbamylphosphate synthetase deficiency (CPS) (citrulline or arginine supplementation required)Ornithine transcarbamylase deficiency (OTC) (citrulline or arginine supplementation required)Citrullinemia or argininosuccinic acid synthetase deficiency (AS) (arginine supplementation required)Argininosuccinic acid lyase deficiency (AL) (arginine supplementation required)Arginase deficiencyIngredients:L-Amino Acids (L-Lysine Acetate, L-leucine, L-phenylalanine, L-valine, L-isoleucine, L-methionine, L-threonine, L-histidine, L-tryptophan), sugar, potassium phosphate, calcium phosphate, calcium carbonate, salt, choline bitartrate, m-inositol, ascorbic acid, ferrous sulfate, vanillin, niacinamide, vitamin E acetate, zinc sulfate, calcium-D-pantothenate, copper acetate, pyridoxine hydrochloride, Thiaminee hydrochloride, riboflavin, manganese, Sulfate, vitamin A acetate, biotin, folic Acid, potassium iodide, vitamin K1, ammonium heptamolybdate, vitamin D3, vitamin B12Precautions:Use only under strict medical supervision. Not for use when planning or during pregnancy.Seek medical advice before using with serotonergic medications.; 500 g / 17.6 oz; 6 Each / Case | |